[A case of multiple myeloma with diffuse parenchimatous alveoloseptal amyloidosis].
نویسندگان
چکیده
概 要IgG(λ)型 多 発性 骨髄腫 に合併 した びまん性肺胞 中隔 型肺 ア ミロ イ ド症 の1症 例 を報告 した.こ の まれ な多発 性骨 髄腫 にお け る肺 ア ミロイ ド症 の病 態 にっい て考 察 した.症 例.59才, 男性.主 訴,労 作時 呼吸 困難.胸 部X線 写真上,全 肺 野 にび まん性小 粒状陰 影 を認 め る.骨X線 像 では,左 上腕 骨 に打 ち抜 き像,骨 髄 中骨 髄腫細 胞24%,2.3g/dlのlg(x(λ)型M成 分,Bence Jones蛋 白陰性,肺 機 能検 査 ではDLCO著 減(%DLCO52%)を 示 した.肺 生検像 で は,単 ク ロ一 ン性形 質細 胞,す なわ ち骨 髄腫 細胞 の浸潤 と,肺 胞 壁,小 血管壁 の アミロイ ド沈着 を証明 した.メ ル フ ァラ ン,プ レ ドニ ゾロ ンの 治療 に よ り軽快 した.
منابع مشابه
A Rare Presentation of Multiple Myeloma: A Case Report of Hepatic Amyloidosis
The clinically reported case of liver involvement with multiple myeloma (MM) is rare. Amyloidosis, defined as a tissue deposition of clonal light-chain fibrils, has been reported in 10-15% of the MM patients. We described a rare MM patient with the primal presentation of fulminant hepatic failure and biliary system involvement due to amyloidosis. Our patient had the primal symptoms of hyperbili...
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عنوان ژورنال:
- Nihon Naika Gakkai zasshi. The Journal of the Japanese Society of Internal Medicine
دوره 75 7 شماره
صفحات -
تاریخ انتشار 1986